Heterotaxy with malrotation is a rare. The details of understanding the anatomy and embryology are challanging, even for many physicians. A simplified explanation is that heterotaxy is a partial situs inversus. In situs inversus, the abdominal organs are in a complete mirror image placement within the abdomen. Partial reversal is termed “heterotaxy or heterotaxia.” Heterotaxy may be associated with malrotation. The decision when to evaluate a patient with heterotaxy for malrotation is discussed in the PowerPoint presentation below.
The following pdf gives details of the disorder for medical professionals and includes surgical photos.